Klippel-Trenaunay-Weber syndrome with intracranial dural arteriovenous fistula and spinal arteriovenous shunt
Abstract
Our clinical image revealed a case of Klippel-Trenaunay-Weber syndrome (KTWS) accompanied by a spinal arteriovenous shunt and an intracranial dural arteriovenous fistula. There have been few reports of KTWS patients developing dural arteriovenous fistulas. This clinical image highlights the strong association between KTWS and CNS vascular malformations. It is important to note that KTWS patients are at risk of developing central nervous system vascular diseases. Therefore, early detection and screening are recommended.
Keywords:
Klippel-Trenaunay-Weber Syndrome
Dural Arteriovenous Fistula
Spinal Vascular Malformation
Angiography
Section
References
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How to Cite
“Klippel-Trenaunay-Weber Syndrome With Intracranial Dural Arteriovenous Fistula and Spinal Arteriovenous Shunt ”. Human Brain, vol. 2, no. 3, Aug. 2023, https://doi.org/10.37819/hb.3.1786.
How to Cite
“Klippel-Trenaunay-Weber Syndrome With Intracranial Dural Arteriovenous Fistula and Spinal Arteriovenous Shunt ”. Human Brain, vol. 2, no. 3, Aug. 2023, https://doi.org/10.37819/hb.3.1786.
Funding data
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Natural Science Foundation of Beijing Municipality
Grant numbers 82101369
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Copyright (c) 2023 Xin Su, Yongjie Ma, Hongqi Zhang, Guilin Li, Jingwei Li
This work is licensed under a Creative Commons Attribution-NoDerivatives 4.0 International License.
